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KMID : 1143020180230030184
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Archives of Hand and Microsurgery
2018 Volume.23 No. 3 p.184 ~ p.189
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Surgical Treatment of Syndactyly of Harlequin Ichthyosis
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Ahn Sung-Jae
Hong Jong-Won
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Abstract
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Harlequin ichthyosis (HI) is a rare and most severe form of autosomal recessive congenital ichthyoses characterized by excessive hyperkeratosis. The skin anomalies affect the shape of eyes, ears, nose, mouth, and distal extremities. Since HI is very fatal, there is a lack of data that documents successful treatment of HI patients with syndactyly. We successfully managed syndactyly in a HI patient by using a conventional method without any complication and we noticed an improvement functionally and aesthetically.
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KEYWORD
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Lamellar ichthyosis, Syndactyly, Hand deformities, Skin transplantation
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Listed journal information
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